Item Type | Name |
Concept
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Hemangioma, Cavernous, Central Nervous System
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Academic Article
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A founder mutation as a cause of cerebral cavernous malformation in Hispanic Americans.
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Academic Article
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Ultrastructural pathological features of cerebrovascular malformations: a preliminary report.
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Academic Article
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Multilocus linkage identifies two new loci for a mendelian form of stroke, cerebral cavernous malformation, at 7p15-13 and 3q25.2-27.
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Academic Article
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Endothelial cell culture from human cerebral cavernous malformations.
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Academic Article
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Variations in structural protein expression and endothelial cell proliferation in relation to clinical manifestations of cerebral cavernous malformations.
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Academic Article
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Multiple spinal cavernous malformations with atypical phenotype after prior irradiation: case report.
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Academic Article
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Biallelic somatic and germ line CCM1 truncating mutations in a cerebral cavernous malformation lesion.
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Academic Article
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Spectrum of genotype and clinical manifestations in cerebral cavernous malformations.
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Academic Article
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Advanced magnetic resonance imaging of cerebral cavernous malformations: part II. Imaging of lesions in murine models.
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Academic Article
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Oligoclonal immune response in cerebral cavernous malformations. Laboratory investigation.
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Academic Article
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Cerebral cavernous malformations proteins inhibit Rho kinase to stabilize vascular integrity.
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Academic Article
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A novel mouse model of cerebral cavernous malformations based on the two-hit mutation hypothesis recapitulates the human disease.
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Academic Article
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A founder mutation in the Ashkenazi Jewish population affecting messenger RNA splicing of the CCM2 gene causes cerebral cavernous malformations.
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Academic Article
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Concepts and hypotheses: inflammatory hypothesis in the pathogenesis of cerebral cavernous malformations.
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Academic Article
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Cavernous malformations.
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Academic Article
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Cerebral cavernous malformations: somatic mutations in vascular endothelial cells.
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Academic Article
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Fatal "hypertensive" intracerebral hemorrhage associated with a cerebral cavernous angioma: case report.
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Academic Article
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Fasudil decreases lesion burden in a murine model of cerebral cavernous malformation disease.
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Academic Article
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Magnetic resonance imaging evaluation of cerebral cavernous malformations with susceptibility-weighted imaging.
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Academic Article
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Cerebral cavernous malformations: clinical insights from genetic studies.
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Academic Article
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Mapping a gene causing cerebral cavernous malformation to 7q11.2-q21.
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Academic Article
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Brainstem cavernous malformations.
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Academic Article
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Cerebral cavernous malformations as a disease of vascular permeability: from bench to bedside with caution.
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Academic Article
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Genetic heterogeneity of inherited cerebral cavernous malformation.
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Academic Article
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Advanced magnetic resonance imaging of cerebral cavernous malformations: part I. High-field imaging of excised human lesions.
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Academic Article
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Immune response in human cerebral cavernous malformations.
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Academic Article
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Biology of vascular malformations of the brain.
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Academic Article
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Intracranial cavernous angioma: a practical review of clinical and biological aspects.
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Academic Article
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Cerebral cavernous malformations and epilepsy.
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Academic Article
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Unfolding knowledge on cerebral cavernous malformations.
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Academic Article
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Emerging clinical imaging techniques for cerebral cavernous malformations: a systematic review.
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Academic Article
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What genes can teach us about human cerebrovascular malformations.
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Academic Article
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Evaluation of iron content in human cerebral cavernous malformation using quantitative susceptibility mapping.
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Academic Article
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Immune complex formation and in situ B-cell clonal expansion in human cerebral cavernous malformations.
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Academic Article
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Exceptional aggressiveness of cerebral cavernous malformation disease associated with PDCD10 mutations.
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Academic Article
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Dynamic permeability and quantitative susceptibility: related imaging biomarkers in cerebral cavernous malformations.
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Academic Article
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Lesions from patients with sporadic cerebral cavernous malformations harbor somatic mutations in the CCM genes: evidence for a common biochemical pathway for CCM pathogenesis.
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Academic Article
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Vascular permeability in cerebral cavernous malformations.
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Academic Article
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Peripheral plasma vitamin D and non-HDL cholesterol reflect the severity of cerebral cavernous malformation disease.
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Academic Article
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Cerebral cavernous malformations arise from endothelial gain of MEKK3-KLF2/4 signalling.
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Academic Article
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B-Cell Depletion Reduces the Maturation of Cerebral Cavernous Malformations in Murine Models.
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Academic Article
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Quantitative Susceptibility Mapping in Cerebral Cavernous Malformations: Clinical Correlations.
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Academic Article
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Micro-computed tomography in murine models of cerebral cavernous malformations as a paradigm for brain disease.
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Academic Article
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Corrigendum: Cerebral cavernous malformations arise from endothelial gain of MEKK3-KLF2/4 signalling.
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Academic Article
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RhoA Kinase Inhibition With Fasudil Versus Simvastatin in Murine Models of Cerebral Cavernous Malformations.
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Academic Article
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Vascular permeability and iron deposition biomarkers in longitudinal follow-up of cerebral cavernous malformations.
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Academic Article
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Endothelial TLR4 and the microbiome drive cerebral cavernous malformations.
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Academic Article
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The cerebral cavernous malformation disease causing gene KRIT1 participates in intestinal epithelial barrier maintenance and regulation.
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Academic Article
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Thrombospondin1 (TSP1) replacement prevents cerebral cavernous malformations.
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Academic Article
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Quantitative susceptibility mapping as a monitoring biomarker in cerebral cavernous malformations with recent hemorrhage.
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Academic Article
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Phenotypic characterization of murine models of cerebral cavernous malformations.
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Academic Article
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Cerebral cavernous malformations form an anticoagulant vascular domain in humans and mice.
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Academic Article
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Trial Readiness in Cavernous Angiomas With Symptomatic Hemorrhage (CASH).
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Academic Article
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Plasma Biomarkers of Inflammation Reflect Seizures and Hemorrhagic Activity of Cerebral Cavernous Malformations.
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Academic Article
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Atorvastatin Treatment of Cavernous Angiomas with Symptomatic Hemorrhage Exploratory Proof of Concept (AT CASH EPOC) Trial.
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Academic Article
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Plasma Biomarkers of Inflammation and Angiogenesis Predict Cerebral Cavernous Malformation Symptomatic Hemorrhage or Lesional Growth.
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Academic Article
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Rho Kinase Inhibition Blunts Lesion Development and Hemorrhage in Murine Models of Aggressive Pdcd10/Ccm3 Disease.
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Academic Article
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Comprehensive transcriptome analysis of cerebral cavernous malformation across multiple species and genotypes.
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Academic Article
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A conserved CCM complex promotes apoptosis non-autonomously by regulating zinc homeostasis.
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Academic Article
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Transcriptome clarifies mechanisms of lesion genesis versus progression in models of Ccm3 cerebral cavernous malformations.
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Academic Article
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Distinct cellular roles for PDCD10 define a gut-brain axis in cerebral cavernous malformation.
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Academic Article
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Cerebral Cavernous Malformation Proteins in Barrier Maintenance and Regulation.
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Academic Article
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Stereotactic laser interstitial thermal therapy for epilepsy associated with solitary and multiple cerebral cavernous malformations.
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Academic Article
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Subclinical imaging changes in cerebral cavernous angiomas during prospective surveillance.
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Academic Article
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Antibodies in cerebral cavernous malformations react with cytoskeleton autoantigens in the lesional milieu.
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Academic Article
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Common transcriptome, plasma molecules, and imaging signatures in the aging brain and a Mendelian neurovascular disease, cerebral cavernous malformation.
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Academic Article
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Cerebral cavernous malformations are driven by ADAMTS5 proteolysis of versican.
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Academic Article
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Novel Murine Models of Cerebral Cavernous Malformations.
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Academic Article
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Propranolol inhibits cavernous vascular malformations by ß1 adrenergic receptor antagonism in animal models.
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Academic Article
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A Roadmap for Developing Plasma Diagnostic and Prognostic Biomarkers of Cerebral Cavernous Angioma With Symptomatic Hemorrhage (CASH).
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Academic Article
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PIK3CA and CCM mutations fuel cavernomas through a cancer-like mechanism.
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Academic Article
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Abortive intussusceptive angiogenesis causes multi-cavernous vascular malformations.
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Academic Article
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Astrocytes propel neurovascular dysfunction during cerebral cavernous malformation lesion formation.
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Academic Article
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Cerebral Cavernous Malformation: From Mechanism to Therapy.
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Academic Article
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Commentary: Feasibility and Morbidity of Magnetic Resonance Imaging-Guided Stereotactic Laser Ablation of Deep Cerebral Cavernous Malformations: A Report of 4 Cases.
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Academic Article
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COVID-19 in a Hemorrhagic Neurovascular Disease, Cerebral Cavernous Malformation.
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Academic Article
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Baseline Characteristics of Patients With Cavernous Angiomas With Symptomatic Hemorrhage in Multisite Trial Readiness Project.
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Academic Article
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Developmental venous anomalies are a genetic primer for cerebral cavernous malformations.
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Academic Article
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Propranolol as therapy for cerebral cavernous malformations: a cautionary note.
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Academic Article
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Rapamycin in Cerebral Cavernous Malformations: What Doses to Test in Mice and Humans.
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Academic Article
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Circulating Plasma miRNA Homologs in Mice and Humans Reflect Familial Cerebral Cavernous Malformation Disease.
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Academic Article
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ß1 integrin monoclonal antibody treatment ameliorates cerebral cavernous malformations.
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Academic Article
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Credulity of exploratory trials for cerebral cavernous malformations.
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Grant
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Rock Inhibition as Therapy for Cerebral Cavernous Malformation
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Grant
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IMMUNE RESPONSE IN HUMAN CEREBRAL CAVERNOUS MALFORMATIONS
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Grant
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Genesis and Progression of Cerebral Cavernous Malformations
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Grant
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Development of BA-1049 for treatment of cerebral cavernous malformation
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Grant
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BIOMARKERS OF BRAIN PERMEABILITY IN HUMAN CEREBRAL CAVERNOUS MALFORMATIONS
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Academic Article
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Impact of socioeconomics and race on clinical follow-up and trial enrollment and adherence in cerebral cavernous malformation.
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Academic Article
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mTORC1 Inhibitor Rapamycin Inhibits Growth of Cerebral Cavernous Malformation in Adult Mice.
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Academic Article
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Corrigendum to "Antibodies in cerebral cavernous malformations react with cytoskeleton autoantigens in the lesional milieu" [J. Autoimmun. 113 (2020) 102469].
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Academic Article
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Inflammatory Mechanisms in a Neurovascular Disease: Cerebral Cavernous Malformation.
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Academic Article
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Single-nucleus DNA sequencing reveals hidden somatic loss-of-heterozygosity in Cerebral Cavernous Malformations.
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Academic Article
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Trial Readiness of Cavernous Malformations With Symptomatic Hemorrhage, Part II: Biomarkers and Trial Modeling.
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Academic Article
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Trial Readiness of Cavernous Malformations With Symptomatic Hemorrhage, Part I: Event Rates and Clinical Outcome.
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Academic Article
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Role of Rho-Associated Kinase in the Pathophysiology of Cerebral Cavernous Malformations.
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Academic Article
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Transcriptomic signatures of individual cell types in cerebral cavernous malformation.
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Academic Article
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Antithrombotic Therapy in Cerebral Cavernous Malformations: A Systematic Review, Meta-Analysis, and Network Meta-Analysis.
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